TY - JOUR AU - Mitsiakos, Georgios AU - Drogouti, Eftychia AU - Drogouti, Maria AU - Doitsidis, Charalampos AU - Pazarli, Elisabeth AU - Spyridakis, Ioannis PY - 2017/12/05 Y2 - 2024/03/29 TI - Congenital intestinal lymphangiectasia. A case report JF - Journal of Pediatric and Neonatal Individualized Medicine (JPNIM) JA - J Pediatr Neonat Individual Med VL - 7 IS - 1 SE - DO - 10.7363/070106 UR - https://jpnim.com/index.php/jpnim/article/view/070106 SP - e070106 AB - Congenital intestinal lymphangiectasia, first described by Waldmann et al. in 1961, is a rare congenital malformation of the lymphatics, presented with generalized edema, hypoproteinemia and lymphopenia. Diagnosis is based on endoscopy findings and pathology.<br />We present here a case of a male neonate, second child of an indigenous woman, delivered by caesarean section. Prenatally, multiple cystic abdominal masses were identified by ultrasound. The patient was treated successfully with enterectomy and anastomosis. Histopathology revealed primary intestinal lymphangiectasia with no features of malignancy.<br />Intestinal lymphangiectasia is a rare pathology, which should be differentiated while exploring abdominal masses, hypoproteinemia and edema especially in neonates. ER -